A Case of the Kugelberg-Welander Syndrome Complicated with Cardiac Lesions

Shinichi KIMURA; Hiromitsu YOKOTA; Kunihiko TATEDA; Kenji MIYAMOTO; Koji YAMAMOTO; Junichi SHIBATA

doi:10.1536/ihj.21.417

Shinichi KIMURA, Hiromitsu YOKOTA, Kunihiko TATEDA, Kenji MIYAMOTO, Koji YAMAMOTO, Junichi SHIBATA

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Keywords: Muscle atrophy, Cardiomegaly, Atrial standstill, Junctional escape rhythm

JOURNAL FREE ACCESS

1980 Volume 21 Issue 3 Pages 417-422

DOI https://doi.org/10.1536/ihj.21.417

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Abstract

There have been a few reports of cardiac involvement in the Kugelberg-Welander syndrome. We presented a case of this syndrome complicated with cardiomegaly and conduction disturbance. The patient, a 21-year-old woman, had atrial standstill and A-V junctional rhythm. The chest X-ray film showed marked cardiomegaly. The His bundle electrogram revealed that H-V interval was 40 msec. She was treated with implantation of cardiac pacemaker.

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