Abstract
A 40-year-old man with combination of left ventricular-right atrial communication and an aneurysm of the atrioventricular membranous septum is presented. A supravalvular type defect, 14×15mm in size, was closed with a Teflon patch. An oval shaped aneurysm of the atrioventricular membranous septum, 20×17mm in size was also noted, but was left untouched. To our knowledge, this is the first reported case with this combination in Japan.