Abstract
A fibromyxoma is a rare odontogenic mesenchymal tumor of the jaws. It is benign and painless but locally destructive. The mandible is more commonly involved than the maxilla. Its histological and radiological features make a fibromyxoma difficult to differentiate from other odontogenic tumors and it may occasionally be misinterpreted as a malignant lesion. In this paper, we present an aggressive case of a fibromyxoma of the maxilla with radiological consideration, postoperative follow-up, and a brief review of the literature.