Intractable & Rare Diseases Research
Online ISSN : 2186-361X
Print ISSN : 2186-3644
ISSN-L : 2186-3644
A rare challenge in general surgery: double surgical procedure for large and small bowel obstruction in a patient with Gerstmann-Sträussler-Scheinker syndrome
Andrea CostanziMichela MonteleoneValter BerardiAngelo MirandaGiulio MariDario Maggioni
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2021 Volume 10 Issue 1 Pages 52-54


Gerstmann-Sträussler-Scheinker syndrome (GSS) is a rare, infectious syndrome related to a mutation in the prion protein gene. Described here are the challenges posed by surgery for a patient with GSS. A 61-yr-old woman with GSS was admitted to this department and underwent surgery twice for large and small bowel obstruction. This is the first report of two major surgical procedures in a patient with GSS. Experiences with this case and precautions when using a disposable device during endotracheal intubation and a surgical procedure to manage a patient with GSS are described.

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© 2021 International Research and Cooperation Association for Bio & Socio-Sciences Advancement
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