Abstract
A case of primary pulmonary hypertension with the aneurysm of pulmonary trunk was reported. The patient is 38 years old house wife with chief complaints of hemoptysiss and exertional dyspnea for 9 years duration. The findings of chest X-ray, EKG and physical examination were compatible with the primary pulmonary hypertension. Graham Steel diastolic murmur was heard at the left sternal border in 3rd, intercostal space. Cardiac catheterization on admission in Feb., 1963 revealed marked . high pulmonary arterial pressure with normal left atrial pressure and no evidence of intracardiac shunt, Angiocardiography confirmed the diagnosis of the aneurysm of pulmonary trunk. Following the administration of Nialamide (Monoamine Oxidase Inhibitor) 75mg in doses for 2 months, patient was recatheterized, and this test revealed moderate decrease of pulmonary arterial pressure with some improvement of subjective symptoms. Since then the patient has been placed on Nialamide and Persantin, At present she is still alive but her condition became worse with signs of right ventricular failure.
In discussion, review of the literatures concerning the primary pulmonary hypertension and the aneurysm of pulmonary trunk was made particularly in reference to their etiologic factors, differential diagnosis and treatment. The importance of differential diagnosis was stressed, since the exploratory cardiotomy for this condition usually terminate the disastrousresult, Two our own cases were presented with the signs and symptoms simulating this present case, However, angiocardiography revealed the presence of ventricular septal defect in one case, and the catheter was inserted in _the left atrium through the atrial septal defect in the other case.
