Abstract
Two cases of progressive facial hemiatrophy are presented.
Case 1.-A 37-years-old female had been in good health until the age of 34 when she first noticed a hollow in her left cheek. Since then this hollow has gradually developed.
Examination revealed atrophy on the left side of her face most noticeably over the cheek and wasting of the left side of the tongue. It also disclosed anisocoria, the left pupil being slightly larger than the right. The EEG revealed low voltage 9-10 per second activity in all areas with bursts of 4-5 per second bilaterally synchronous high voltage wave and disorganized spike&wave complex in the anterior part of the head. Minor's test revealed slight diminution of the sweat secretion on the left side of her face.
Case 2.-A 30-years-old female noticed an indentation in her right forehead and cheek, two years prior to examination, which since then has slowly increased in depth. The skin overlying the affected area in her right forehead was brown, which had been noticed since her childhood.
Examination revealed atrophy on the right side of her face and brown pigmented area on her right forehead. No other abnormality was presented on the physical examination, The EEG presented low voltage 8-9 per second activity in all areas with some sporadic or rhythmic, moderate voltage 7 per second activity in the anterior part of the head.
The etiology in progressive facial hemiatrophy was discussed and the trophoneurosis theory was supported.