Abstract
A case of the autoimmune hepatitis which developed four months after the renal tubular acidosis was reported. The autoimmune mechanism was considered to be the common cause of both disorders.
A 32-year-old woman was admitted to our hospital because of hypovolemic shock, hypokalemia and hyperchloremic acidosis, and the tentative diagnosis of renal tubular acidosis of unknown cause was made. She improved with oral administration of Indomethacin.
Three months after discharge, she developed autoimmune hepatitis, and improved with plasma exchange and steroid therapy.
The clinical course of this case was defferent from usual autoimmune hepatitis with renal tubular acidosis because autoimmune hepatitis developed four months after the renal tubular acidosis.