Abstract
Four patients with pulmonary arteriovenous fistula (PAVF) were treated for the past ten years. Examinations of their families revealed Osler's disease (hereditary hemorrhagic telangiectasia) in all. In the four families, another three cases of PAVF were found. Of these seven patients with PAVF, only three underwent surgery. Of four unoperated patients, one died of brain abscess ten months after the diagnosis, one suffered from cerebrovascular accident one year after the diagnosis.