Abstract
We present 3 cases of DMD. The disease developed at their infant period in all 3 cases. They were admitted at 4-9 years old. They fell in stage V at 9-10 years old. The height and body weight were small compared with normal children. Vital capacity had been progressively decreased to 610±25 cc at their terminal stages and tracheotomy was done in 2 cases.
CPK, LDH, Aldolase, GOT, GPT showed high values in the beginning of the disease, and they decreased gradually with the progression of the disease. PaO2, PaCO2 demonstrated abnormal values and the patients fell into a delirious state. The serum pH showed respiratory acidosis.
We used several methods including postural drainage, vibrator and, tapping in order to discharge sputum. All of these 3 cases died of respiratory insufficiency, pneumonia and bleeding from tracheo-arterial fistula, respectively.