Abstract
We report two families of benign infantile convulsions (BIC) proposed by Fukuyama in 1963. Despite Fukuyama's definition, in which BIC was said to be nonfamilial, several reports of BIC with familial occurrence have been published. Kajiyama first described a clinical entity of BIC with familial aggregation and named “familial BIC” in 1987. Together with previous reports and the present experience, the characteristics of familial BIC were summarized as follows. (1) Familial occurrence is noted. (2) The age of onset is from 3 to 5 months old. (3) Convulsion occurs without any precipitating factors such as gastroenteritis and upper respiratory infection. (4) Convulsion has a tendency to occur in clusters within a day. (5) In the same family, the onset of age and the incidence of attack are similar.