Abstract
Case. In February 2008, a 57-year-old woman was referred to our hospital for the investigation of an abnormal shadow detected on a chest radiograph and an increased serum CA19-9 level. Computed tomography revealed a tumor in the left dome of the diaphragm; the tumor showed fluorodeoxyglucose (FDG) uptake on FDG-positron-emission tomography (PET). During tumor resection, an aberrant artery was found to supply the tumor, which was diagnosed as an extralobar pulmonary sequestration and resected. After the operation, the serum CA19-9 level decreased. Conclusion. We have reported a rare case of extralobar pulmonary sequestration presenting with an increased serum CA19-9 level.