Abstract
A 17-year-old girl with chest pain visited our hospital and was diagnosed with left pneumothorax. Chest CT revealed a localized emphysematous area and a small nodule in the left S6 segment with absence of the B6 bronchus. Bronchofiberscopy and MRI confirmed a diagnosis of congenital bronchial atresia accompanied by mucoid impaction. We performed thoracoscopic left S6 segmentectomy because of prolonged air leakage derived from the emphysematous region in the S6 segment that was clearly distinguished from other segments. Pneumothorax due to congenital bronchial atresia is a rare disease. Segmentectomy including the affected region is recommended for similar cases.
