A case of congenital cystic adenomatoid malformation with repeated pulmonary infection in adulthood and review of thirteen cases in Japan

Abstract

We report a 38-year-old woman with congenital cystic adenomatoid malformation (CCAM) type I.

She was admitted to undergo surgery following repeated recurrence on antibiotic therapy. Chest computed tomography showed multiple cystic lesions in the right lower lobe. After the third antibiotic treatment, right lower lobectomy was performed. The histopathological diagnosis was CCAM type I, and small cysts were found near the resection stump of S⁶. Two weeks after surgery, she developed a late-onset pulmonary fistula and was treated with chest tube drainage and pleurodesis. Therefore, it is necessary to pay attention to the extent of cysts and remove them completely.