2022 Volume 36 Issue 5 Pages 590-595
A desmoplastic small round cell tumor (DSRCT) is an extremely rare high-grade tumor that frequently develops in the abdominal cavity of young men. Herein, we report a case of pericardial DSRCT. A woman in her thirties underwent pericardial drainage for congestive heart failure due to cardiac tamponade at a hospital. The pericardial effusion was bloody, and atypical cells were detected on cytology. She was referred to our hospital for a detailed examination. Chest computed tomography revealed a thickened pericardium and large amount of pericardial effusion; however, there was no evidence of the primary lesion. Thoracoscopic pericardial fenestration was performed for tissue collection and drainage of the pericardial effusion. She was histopathologically diagnosed with DSRCT. Although DSRCT has been reported to occur extra-abdominally, this is the first reported case of DSRCT showing pericardial involvement in Japan. There are few atypical cases of DSRCT.
