2000 Volume 14 Issue 2 Pages 172-177
A 32-year-old woman with von Recklinghausen's disease was admitted for the treatment of metastatic lung tumor. She had undergone extended radical tumorectomy, radiotherapy, and chemotherapy for MPNST in right lower limb 33 months ago . Chest X-ray and CT showed a sharply demarcated solitary tumor in the right S6. Resection of the tumor under video-assisted thoracoscopic surgery was performed . The lung tumor was histologically diagnosed as a metastasis of MPNST.
Lung is the most common metastatic site of MPNST and MPNST with lung metastasis showing a very poor prognosis. The patient is well 21 months after the pulmonary resection without recurrence. Multidisciplinary therapy and careful follow up are important for MPNST.
