Abstract
This is a case report of congenital cystic adenomatoid malformation of the lung (CCAM) ininfant with respiratory infection. A female infant, 6 months old, was admitted to hospitalbecause of high fever. Chest X-ray showed infiltrative shadow in the right lower lung field.Chest CT and MRI were performed in our hospital, and showed a mass with multiple cysts inthe right lower lobe. Aberrant arteries were not confirmed by aortography. The patient wasdiagnosed with cystic disease of lung, and right lower lobectomy was performed at 1 year. Theresected lung had multiple small cysts. On histological examination, the cyst wall was lined byciliated columnar epithelium, and bronchial cartilage was absent through out the lesion. So thediagnosis of CCAM was confirmed. Because CCAM has a risk of recurrence, segmentectomyor lobectomy which includes the lesion is recommended in its management.