2017 Volume 66 Issue 1 Pages 74-79
T-lymphoblastic lymphoma (T-LBL) is a malignant tumor of precursor T-lymphocyte origin, which differentiated to T-lymphocytes. The tumor is often formed in lymph nodes or extranodal organs. Respiratory disorder may develop as a complication of mass displacement, and early diagnosis and treatment are necessary. Terminal deoxynucleotidyl transferase (TdT) is usually present in 90–95% of T-LBL patients, and it is used as an essential marker in the diagnosis. We experienced treating a case of TdT-negative T-LBL. LBL is uncommon epidemiologically, and it was atypical to have a TdT-negative case; therefore, it was a very uncommon case. If the case is atypical, it is important to diagnose it comprehensively, which includes the search for other markers and clinical information.
