2023 Volume 32 Issue 11 Pages 746-751
Perivascular epithelioid cell tumor (PEComa) is a rare soft-tissue tumor, with only a few reports of lesions located in the head and neck region. The case we describe here involved a rapidly growing left temporal tumor, which was diagnosed as a malignant PEComa of the left masticatory space. Initially this tumor was considered to be a primary lesion. However, review of a pathologic specimen from a uterine myoma that was resected two years earlier revealed that the temporal tumor was in fact a malignancy due to primary PEComa of the uterus.
In all cases of soft-tissue tumors with a non-intracranial origin, we consider that the diagnosis and treatment may need to be determined on a case-by-case basis by multiple departments rather than neurosurgery alone. Furthermore, when soft-tissue tumors arise in women, clinicians should consider reexamining previous pathologic specimens when the patient has a history of uterine myoma.
