Abstract
We report the case of the youngest patient who has suffered from a rare clear cell meningioma of the thoracic spine. The patient was an 8-year, 6-month-old girl noted with a deteriorating gait and hypesthesia below the S1 level. Magnetic resonance imaging showed an intradural extramedullary tumor at the vertebral level between The 10 and Th 12, which was totally removed using a posterolateral approach (Simpson II). The tumor was attached to the dura mater and dorsal rootlet at the 10th thotacic root exit zone. Pathological findings revealed a glycogen-rich clear cell meningioma with marked stromal hyaline connective tissue. Clear cell meningiomas are a new subtype recognized at the latest World Health Organization Committee of Brain Tumor Pathology. The tumors are characterized by a clear cytoplasm containing abundant glycogen and numerous stromal hyalinized collargen deposits. It has diverse clinical characteristics compared to typical meningiomas, such as a younger onset (less than 40-year-old), no sex predilection, frequent spinal intradural occurrence especially the lumbar region, and frequent local recurrence and metastases. Clear cell meningioma is rare but important clinically as a subtype of spinal meningioma.
