Abstract
Extraskeletal myxoid chondrosarcoma (EMC) is a rare soft tissue sarcoma that is considered low-grade. We have treated two cases of EMC.
Case 1: A 46-year-old man with EMC on the left upper arm. We opted for marginal excision and added radiotherapy. Chemotherapy was performed for pulmonary metastasis. After ten years and there is no evidence of local recurrence or metastasis.
Case 2: A 65-year-old man with EMC on the left thigh. There was neither local recurrence nor metastasis six months after surgery with wide excision.
The clinical behavior of EMC is considered to be that of a low-grade sarcoma, based on the first description of the tumor by Enzinger and Shiraki, who reported that only 4 out of 34 patients died of the disease within a short-term follow-up period (median 3.5 years). Later, in 1992, Saleh et al. followed up ten patients with EMC over a long period and concluded that EMC is a persistent and finally devastating tumor with a high potential for local recurrence and distant metastasis, despite showing an indolent long-term course. We must consider the possibility of recurrence and metastasis after long-term progression of EMC, and therefore prudent follow-up is required.
