A case of progressive hearing loss due to congenital cytomegalovirus infection complicated by congenital cholesteatoma

Abstract

Congenital cytomegalovirus (cCMV) infections can cause congenital or progressive hearing loss and delayed language development. However, cCMV has not been reported to be associated with congenital cholesteatoma to date. Our patient was a 4-year-old girl. She was born without any perinatal abnormalities, and she passed a newborn hearing screening (NHS). Cochlear implant surgery and cholesteatoma surgery were performed on two separate occasions. Speech was observed approximately 10 months after surgery. It is important to note that even if newborn passes NHS, cCMV may cause delayed progression of hearing loss and delay the diagnosis of hearing loss.