Abstract
We report a case of SNL presenting with HPS. A 46-year-old female visited our clinic with a high fever and left neck lymphadenopathy. A lymph node biopsy showed a necrotic lesion and an apoptosis body-like figure, thus indicating that she had previously suffered from SNL. Under this diagnosis, we administered steroids (i. v.), however, a high fever and pancytopenia continued and the patient unfortunately died due to an intestinal hemorrhage. Her serum levels of ferritin, LDH and sIL-2R were remarkably elevated. We thus suspected HPS and performed bone marrow aspiration cytology, but the findings did not show any blood-cell phagocytosis figures in the neutrophils. However, the post-mortem findings definitely showed phagocytosis figures in the blood cells.
