CONGENITAL INCUDOSTAPEDIAL DISCONNECTION

SOTARO FUNASAKA; TATSUJIRO USHIJIMA; JUN YANO

doi:10.3950/jibiinkoka.82.476

SOTARO FUNASAKA, TATSUJIRO USHIJIMA, JUN YANO

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JOURNAL FREE ACCESS

1979 Volume 82 Issue 5 Pages 476-482

DOI https://doi.org/10.3950/jibiinkoka.82.476

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Published: May 20, 1979 Received: December 15, 1978 Available on J-STAGE: March 19, 2008 Accepted: - Advance online publication: - Revised: -
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Date of correction: March 19, 2008 Reason for correction: - Correction: ABSTRACT Details: Right : Recent advancement in otomicrosurgery has brought us more chance to find the congenital ossicular malformation without any anomalies of the external ear and we have experienced 18 ears of the congenital ossicular malformations.
This presentation includes the review on surgical correction and the embryogenetic discussions for eight ears of congenital incudostapedial disconnection observed in these 18 congenital ossicular anomalies.
The congenital incudostapedial disconnection was characterized by the absence or deformity of the long crus of the incus and of the superstructure of the stapes which had the mobile footplate without any exceptions.
The embryological studies have shown that the incudostapedial disconnection is resulted from the maldevelopment localized on "the secondary continuity", which is formed between the Ist and IInd branchial arches at sixth week of embryo.
The surgical correction was to connect the malleus handle to the stapes by a silicone tube specially designed or a gelfoam wire in the uncustomary way. The results were quite satisfactory and postoperative hearing has improved to less than 30 dB (JIS standard) in all of the cases, and this fact distinguished the incudostapedial disconnection from other types of the congenital ossicular malformation.
Thus, from both embryological and surgical standpoints of view the congenital incudostapedial disconnection should be dealt with a clinical entity.

Date of correction: March 19, 2008 Reason for correction: - Correction: PDF FILE Details: -

Abstract

Recent advancement in otomicrosurgery has brought us more chance to find the congenital ossicular malformation without any anomalies of the external ear and we have experienced 18 ears of the congenital ossicular malformations.
This presentation includes the review on surgical correction and the embryogenetic discussions for eight ears of congenital incudostapedial disconnection observed in these 18 congenital ossicular anomalies.
The congenital incudostapedial disconnection was characterized by the absence or deformity of the long crus of the incus and of the superstructure of the stapes which had the mobile footplate without any exceptions.
The embryological studies have shown that the incudostapedial disconnection is resulted from the maldevelopment localized on "the secondary continuity", which is formed between the Ist and IInd branchial arches at sixth week of embryo.
The surgical correction was to connect the malleus handle to the stapes by a silicone tube specially designed or a gelfoam wire in the uncustomary way. The results were quite satisfactory and postoperative hearing has improved to less than 30 dB (JIS standard) in all of the cases, and this fact distinguished the incudostapedial disconnection from other types of the congenital ossicular malformation.
Thus, from both embryological and surgical standpoints of view the congenital incudostapedial disconnection should be dealt with a clinical entity.

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