FAMILIAR APEARANCE OF UNILATERAL TOTAL DEAFNESS IN CHILDREN
1987 Volume 90 Issue 12 Pages 1974-1983
Details
1987 Volume 90 Issue 12 Pages 1974-1983
One hundred eighty three family lines with juvenile unilateral total deafness treated in the authors' clinic to children with sensori-neural hearing loss during 15 years from 1970 to 1985 were studied.
Their clinical history and the results of hearing, tomography, caloric tests and pedigree patterns were investigated. A total of 553 relatives were examined for their hearing by the audiometry.
Following results were obtained.
1. In the 183 family lines with juvenile unilateral total deafness, there were 10 cases of 5 family lines (or 2.73%). Their family lines were 3 cousin's families, 1 brother's family and 1 aunt and boy's family. 1 case of 10 cases was found to have inner ear deformity in the side of hearing loss.
2. The total of family lines with sesori-neural hearing loss relatives were 75 family lines (or 41.0%). The family lines with unilateral deafness relatives were 37 (or 20.2%). The family lines with bilateral sesori-neural hearing loss cases were 45 (or 24.6%).
3. The occurring rate of hearing loss in relatives with unilateral total deafness was higher than in normal hearing cases. That rate in lower children was 3-7% (0% in normal hearing cases), and that in the age of 30-40 years old was 14-35% (4-10% in normal hearing cases).
4. Summing up, it may be concluded that the occurrence of unilateral total deafness is related to the hereditary nature, and there are hereditary unilateral total deafness cases.
