A Case of Nasal Dermoplasty for Hereditary Hemorrhagic Telangiectasia

Abstract

Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant genetically transmitted disease characterized by a systemic disorder of the blood vessels. Epistaxis is usually the most common symptom. Nasal dermoplasty is regarded as the effective treatment for moderate to severe cases.
We report on a 71-year-old man with HHT and a large septal perforation who was treated with nasal dermoplasty. Postoperatively, he has shown reduction in the frequency and severity of his epistaxis.