Treatment Outcomes of Patients with Congenital Cholesteatoma

Abstract

We present the treatment outcomes of 17 patients (17 ears) with congenital cholesteatoma who underwent tympanoplasty at our department between April 2004 and September 2019. Tympanoplasty type I was performed in 7 of 17 ears, and staged tympanoplasty was selected for the remaining 10 ears (Type IIIc: 3 ears; Type IIIi-I: 1 ear; Type IVc: 3 ears; Type IVi-M: 3 ears).

The overall success rate of hearing improvement, according to the criteria of the Otological Society of Japan (2010), was 82.4% (14 of 17 ears). Residual recurrence was found in 2 ears treated by Type-I tympanoplasty. Residual cholesteatoma was observed during the second operation in 3 of 10 ears treated by staged tympanoplasty. These results indicate the usefulness of staged tympanoplasty for the prevention of residual cholesteatoma.