Abstract
A 63-year-old man had suffered from increasing bilateral conductive hearing loss, left facial nerve palsy and a vestibular disturbance. Proliferative granular lesions were found in the gingiva, the external canal and the middle ear cavity on both sides. Histopathological studies revealed pemphigus vegetans, and the clinical course during and after steroid therapy suggested the Hallopeau type of this disease. It has been reported that phemphigus vegetans is a rare disease which occurs in the mucosa of the oral cavity or the moist regions of the skin. Moreover, no case with ear problems has been reported.
This paper emphasizes the importance of recognizing this rare disease in the E. N. T. area. The pathogenesis of the ear-associated problem is also discussed.