Aggressive Fibromatosis Involving the Paranasal Sinuses; A Case Report

Abstract

Aggressive fibromatosis is a rare tumor, especially in the head and neck region. Although its pathological findings are benign, clinical findings are malignant, which indicate locally expansive growth and bony destruction. We report a case of aggressive fibromatosis which involved the right paranasal sinuses.
A 40-year-old male was hospitalized due to increasing nasal obstruction, right cheek swelling and repeated nasal bleeding. CT scan and MR images showed that the large mass mainly involved the right maxillary sinus, eroded the walls of the sinus and invaded the right orbita, the nasal cavity, the ethmoid sinus, the sphenoid sinus, the inf ratemporal f ossa and the pterygomaxillary space. An excisional biopsy was performed, and the pathological diagnosis was aggressive fibromatosis. Therefore chemotherapy and radiation therapy were performed, but both were ineffective. Finally, total extirpation of the tumor was carried out, and no recurrence has been revealed over the 15 months after the operation.