2000 Volume 93 Issue 5 Pages 357-360
A high jugular bulb is often discovered as an incidental finding during examinations for hearing loss, with the high jugular bulb itself sometimes being the cause of the loss of hearing. One mechanism of conductive hearing loss in association with this anomaly is the obstruction of the round window niche. This has been reported infrequently in the literature, and a bilateral case is very rare.
An 11-year-old boy with bilateral conductive hearing loss was examined, and it was verified that the round window niche was obstructed due to a high jugular bulb. This patient also had malformations of the external, middle and inner ear, and fistulas in his right neck. He also had a history of patent ductus arteriosus and a ventricular septal defect. The operative findings, radiographic and audiometric data are presented.