Fibrous Dysplasia of the Temporal Bone with a Neurinoma of a Facial Nerve

Abstract

A 61-year old female patient with fibrous dysplasia of the temporal bone is reported. She consulted us for hearing loss in the left ear. Stenosis of the external auditory canal caused the conductive hearing loss. CT-scan and scintiscanning using _99mTc-MDP demonstrated fibrous dysplasic change in the left temporal bone. On MRI, a parotid tumor was discovered on the same side as the fibrous dysplasia of the temporal bone.
Surgery was performed on the external auditory canal and the parotid tumor. After creating a new auditory canal, her hearing loss was improved. Pathological diagnosis of a section of the temporal bone showed fibrous dysplasia.
Surgery of the parotid tumor was also performed. We diagnosed it as a neurinoma of the facial nerve by its surgical and pathological findings.
We review the combination of fibrous dysplasia and the neurinoma in the literature. There is a relationship between fibrous dysplasia and Albright's syndrome and Albright's syndrome has also a relationship to neurofibroma. Both neurinoma and neurofibroma are symptoms of Recklinghausen disease. Therefore, there seemed to be a common area among these diseases.