A Case of Aortic Stenosis Secondary to Bicuspid Aortic Valve Associated with Klippel-Feil Syndrome Treated by Aortic Valve Replacement

Abstract

A 52-year-old male was diagnosed as having aortic stenosis secondary to a bicuspid aortic valve associated with Klippel-Feil syndrome. Aortic valve replacement was successfully performed without any problems in the surgical or anesthesiological management. Only five such cases including ours, who underwent cardiac surgery have been reported. It is possible to perform cardiac surgery for patients with Klippel-Feil syndrome of their cardiac function can be well preserved.