2023 Volume 51 Issue 2 Pages 42-44
Oculodentodigital dysplasia (ODDD) is an autosomal dominant syndrome in which multiple malformations of the face, eyes, fingers, and teeth are observed. Although Hallermann-Streiff syndrome is similar to this disease, the pathology is different. ODDD can be discriminated by the identification of specific genes and syndactyly. Here, we report a 4-year-old boy with ODDD who underwent dental treatment under general anesthesia.
Lateral cranial X-rays showed micrognathia and the tonsillar enlargement. Anesthesia management was conducted via slow induction and was maintained using remifentanil and propofol. A tracheal tube was placed through the nasal cavity using a fiberscope because of the anticipated difficulty of tracheal intubation. The patient’s vital signs were stable throughout the operation. He recovered well and was discharged on the next day. In the presently reported patient with ODDD, a specific risk of general anesthesia was the difficulty in airway management. For patients with suspected micrognathia, lateral head X-rays are likely to be useful for assessing the difficulty of airway management in children and/or patients with intellectual disability, since such images are relatively easy to obtain and provide useful information.
