Abstract
A 63-year-old woman had been observed for a hepatic cyst for about 8 months. In June, 2009, her CA19-9 level was found to be elevated and she was admitted to our hospital. Abdominal ultrasonography (US), computed tomography (CT) and magnetic resonance imaging (MRI) showed a multilocular cystic tumor in the left lobe of the liver, and they showed a partial wall thickening in the cystic tumor. Fluorodeoxyglucose positron emission tomography (FDG-PET) showed uptake in the cystic tumor. Biliary cystadenocarcinoma was diagnosed and left lobectomy of the liver was performed. Macroscopic findings showed the cystic tumor to be composed of blood and mucin, and wall thickening. Histopathologically, the tumor was cystadenocarcinoma with ovarian-like stroma. The postoperative course was uneventful and she is alive without recurrence for 12 months after surgery. Since biliary cystadenocarcinoma with ovarian-like stroma are rare, we report this case with a review of the literature.