Congenital Anomaly of the Intrahepatic Portal System Complicated by Intrahepatic Cholangiocellular Carcinoma-A Case Report

Abstract

Recent progress in diagnostic imaging such as ultrasonography, computed tomography and percutaneus transhepatic portography, allows better comprehension of the anatomy of the intrahepatic portal and venous systems. We report here a patient with an abnormal intrahepatic portal system; cul-de-sac-like dilatation of the right anterior portal vein coming off from the left portal vein, agenesis of the umbilical portion of the left portal vein and the development of a right hepatic round ligament. This entity most likely originates in abnormal development of the fetus. It is indispensable for hepatectomy to understand the intrahepatic portal system as seen in diagnostic modalities.