Abstract
We report a case of malignant peripheral nerve sheath tumor (MPNST) at the ethmoid sinus. A 64-year-old man visited our hospital because of protrusion of his left eye. MRI scan revealed that a tumor of the ethmoid sinus had invaded the left eye socket and the bone at the skull base. Pathological examination revealed that the tumor was MPNST. We resected the tumor including the left eyeball and skull base bone. After resection, we reconstructed his left eye socket for an ocular prosthesis with a free flap.