Case Report: Surgical Treatment of Crouzon Syndrome Compromised with Obstructive Sleep Apnea

Abstract

We report a patient with Crouzon syndrome and obstructive sleep apnea-hypopnea syndrome (OSAHS) treated by the Rigid External Distraction II System (RED II). The patient was an 18-year-old male. He was previously diagnosed with OSAHS in another hospital and was referred for continuation of treatment of OSAHS after changing his address. In the initial polysomnography (PSG) conducted in our hospital, the apnea-hypopnea index (AHI) was 55.9 events/hour, indicating severe OSAHS. The patient was also diagnosed with Crouzon syndrome based on facial malformation and abnormal form of craniofacial bone. For treatment, we selected bone distraction using the RED II after Le Fort III osteotomy, in order to widen the nasal airway and improve facial malformation and masticatory dysfunction. In this case, the bone distraction procedure was continued for 1 month. The treatment improved physiognomy and occlusion and reduced AHI to 25.9 events/hour after distraction.