Abstract
We herein report a case of a 21-year-old female patient treated for fibrodysplasia ossificans progressiva. The symptoms of the disease first appeared at age 6 and was diagnosed as fibrodysplasia ossificans progressiva by biopsy at the age of 7. Trismus appeared at age 12 and ossification progressed gradually. In September 2001, she visited her oral surgeon due to severe tooth pain in the lower right region of the first molar. The surgeon suggested (recommended) surgical transection of the bony fusion as treatment for trismus under general anesthesia. The patient was referred to our clinic for a second opinion. In account of her poor general condition and diminishing reserve capacity, it was impossible to administer general anesthesia. After obtaining informed consent, the tooth was extracted under local anesthesia. At present, the patient's postoperative course of recovery is stable and uneventful.
This case underlines the importance of understanding both the patient's systemic disease and general condition during the course of treatment.
