Article ID: JJMU.A.250
Cor triatriatum (CT) is a rare congenital heart disease (CHD) that accounts for about 0.1-0.4% of CHD cases. It causes various clinical symptoms due to an abnormal septum in the right or left atrium. Atrial fibrillation occurs in about 30% of all CT patients. We describe a case of an adult male who presented with symptomatic CT sinister. He had paroxysmal atrial fibrillation, and he was incidentally diagnosed with CT sinister based on transesophageal echocardiography performed for preoperative workup for catheter ablation. In patients with CT, other CHDs such as partial anomalous pulmonary venous connection or atrial septal defect often coexist. In addition, the abnormal septum may cause obstruction of catheter passage. We carefully considered whether extensive encircling pulmonary vein isolation (EEPVI) could be safely performed. He had no other CHDs, and his abnormal septum was located in the lower atrial septum. Thus, we performed EEPVI without complication using intracardiac echocardiography for transseptal puncture. It is important to consider whether catheter ablation can be safely performed using various modalities. We described a case of CT with paroxysmal atrial fibrillation.
