Abstract
A hemophilic pseudotumor was found in the mandible a of a 13-year-old boy with a known history of moderate hemophilia A.
Intraorally, the alveolus was enlarged buccally and lingually in the left retromolar region. Hypesthesia of the left mental region was noted. Panoramic X-ray film revealed a lytic bone lesion from 7 to the left angle of the mandible.
Computed tomography revealed marked enlargement of the left side of the body of the mandible, associated with a low density area, and irregular absorption of the lingual cortex.
A malignant tumor was suspected, so a biopsy was done during replacement therapy with coagulation factor (Factor VIII). The bone cavity contained a hematoma and was surrounded by granulation-like tissue. A histopathologic diagnosis of hemophilic pseudotumor was made.
One year after curretage, the patient's condition was normal, both clinically and radiologically.
The pathogenetic mechanism was hypothesized to be a pressure-necrosis phenomenon due to intraosseous bleeding.
