Abstract
A melanotic neuroectodermal tumor of infancy (MNTI) is a rare tumor that usually occurs in infants younger than 1 year of age. It is usually benign, only a few reported cases were malignant. MNTI occurs mainly in the maxilla, but can occur in other parts of the skull, the mandible, brain, epididymis, uterus, and mediastinum. To our knowledge, about 10 cases have been reported in the Japanese literature, and most of them arose in the maxilla. We report a case of MNTI arising in the mandible in a 3-week-old boy. Wide resection of the mandible, including the tumor, was performed. The patient has made an uneventful recovery, and there has been no sign of recurrence or metastasis after surgery.
