Long-term observation of basal cell nevus syndrome in a child

Abstract

Basal cell nevus syndrome is a complex disease characterized by multiple cysts of the jaws, multiple basal cell tumors of the skin, and a high incidence of skeletal abnormalities. Jaw cysts often involve permanent teeth in young patients, and we have to preserve permanent teeth whenever possible. We encountered a 9-year-old boy who had multiple jaw cysts and treated him for 9 years. It was possible to preserve the permanent teeth affected by jaw cysts by means of marsupialization. No growth disturbance of the jaws occurred.