A case of renal lymphangiectasia with high-renin hypertension, growth hormone deficiency and polcytemia: 6-year follow up

Abstract

 Renal lymphangiectasia is a very rare disorder in pediatric cystic renal disease. We report a case of renal lymphangiectasia in an 8-year-old boy who presented high-renin hypertension, growth hormone deficiency and polycytemia with increased erythropoietin production. Abdominal ultrasonography showed enlarged kidney with increased echogenicity and poorly defined corticomedullary junctions. MRI reveals low signal intensity on T1-weighted images, which were compatible with the peripelvic cysts. These images are typical of renal lymphangiectasia. This is the first case report that revealed these typical images persistent for 6 years.