A case of unilateral and segmental localized polycystic kidney disease in a boy who was detected at a microscopic hematuria on a school urinary screening

Abstract

Unilateral and segmental localized polycystic kidney disease is a rare, non-familiar, non-progressive renal disorder in other organs. Few cases have been reported in the literature. It is benign nonsurgical condition. Therefore it should be ruled out differential diseases such as autosomal dominant polycystic kidney disease, cystic nephroma, multicular cystic nephroma. To resolve this diagnostic problem needed to perform long-term follow-up. We report a case of a 16 year-old male who detected microscopic hematuria by school urinary screening. He didn’t have any loin pain and abdominal mass and any family history of kidney disease. Ultrasonography showed polycystic kidney at right upper pole kidney, and contralateral kidney was normal. His urine analysis showed microscopic hematuria and his kidney function tests were with in normal range. Computerized tomography showed that there weren’t any disorder in other organs. He has been followed with US study and blood exam for 5 years without surgery. Until now, he was admitted to our hospital because of cyst hemorrhage. We continue following him with Echoic study.