Abstract
Unilateral lung agenesis is extremely rare and have various complications.The onset and clinical course in this disease is quite variable.An 8-month-old boy with severe stridor and wheeze was referred to our hospital to stabilize respiratory failure.He was diagnosed as right lung agenesis with tracheal stenosis.In this case, respiratory management was extremely difficult, but physiotherapy, especially positioning, was very effective.To evaluate precise mechanism, bronchofiberscopy and lung function test were very useful
We speculated that factors leading to serious conditions in this desease are;1) right lung agenesis, 2) compression of trachea by more than 2 blood vessels, 3) complication of tracheal malacia or trachealstenosis, and 4) onset within early infancy.
