A case of Congenital Abscence of Right Main Pulmonary Artery

Abstract

A 24 year-old man was admitted to our hospital with chief complaint of hemoptysis of 10 days duration.
The plane postero-anterior chest roentgenogram revealed the deviation of the mediastinum from left to right, the reticulo-nodular densities in the right lung and hyperaerated lesion in right hilar region.
Macroaggregated, ¹⁸¹I-labeled alubumin lung scan and pulmonary arteriogram showed the abscence of the right pulmonary artery. Thoracic and abdominal aortogram showed abnormally dilated bronchial arteries as collateral circulation. The inhalation lung scan with 99mTc colloid aerosol and bronchogram revealed that hyperaerated lesion was the herniation of the left upper lobe into the right thorax.