Abstract
A 40 year-old female case of primary myxosarcoma of the pulmonary artery was admitted to Kitasato University Hospital with a chief complaint of dyspnea. On physical examination, she appeared chronically ill. The second heart sound at the apex was split and the pulmonic component was loud. Her chest X-ray on admission showed decreased lung volume accompanied by several areas of non-segmental infiltration and prominence of the pulmonary trunk. Her electrocardiogram was compatible with right ventricular hypertrophy. Her 99mTc-MAA perfusion scan indicated massive pulmonary thromboembolisms.
At cardiac catheterization, the following pressures were measured; right atrium 20/10 (mean 15), right ventricle 90/0, pulm. trunk 85/40 (mean 55).
Several vasodilator and anticoagulant agents were prescribed. However, she died due to severe respiratory failure.
At autopsy the pulmonary trunk was found to be filled with tumor which was histologically recognized to be myxosarcoma.
