A case of intrasplenically grown acinar cell carcinoma of the pancreas

Abstract

A 72-year-old man was admitted due to vomiting. Hematological studies revealed only mild anemia. The serum CEA and CA19-9 levels were normal. Abdominal ultrasonography showed a large tumor with several cystic areas in the spleen and swollen lymph nodes along the splenic artery. The tumor occupied most of the spleen. An abdominal CT scan showed enhancement of the tumor bordered by the tail of the pancreas. Angiography showed a hypervascular tumor. Endoscopic examination revealed a submucosal tumor of the stomach and colonic polyps. Given a diagnosis of angiosarcoma arising in the spleen the patient had a distal pancreatectomy, splenectomy, and partial gastrectomy. The histological diagnosis was acinar cell carcinoma of the pancreas with splenic invasion and gastric metastasis. The patient is alive without recurrence 1 year after surgery.