Abstract
We report a case of Peutz-Jeghers syndrome with repeated small intestinal intussusceptions. A 22-year-old woman with small intestinal intussusception underwent surgery and was diagnosed with Peutz-Jeghers syndrome based on family history, oral pigmentation and pathological findings, in 2001. Because of small intestinal intussusception, she underwent small intestinal endoscopy for polypectomy of all but the largest polyp near Treitz's ligament in 2007. However, she was admitted for surgery because of repeated small intestinal intussusceptions in May 2008. Repair of the five small intestinal intussusceptions and endoscopic polypectomy were performed without resection of the small intestine. The postoperative course was uneventful and no further small intestinal intussusceptions occurred. In the case of early detection of recurrences, periodic endoscopic examination is required.