Abstract
A 61-year-old woman complaining of vomiting was diagnosed as having intestinal obstruction at a nearby gastroenterological clinic and underwent i. v. drip infusion therapy in the out-patient clinic. However, no remission was noted so that she was admitted to the hospital and was managed under placement of a long intestinal tube. Thereafter a blood examination revealed BUN of 90.1 mg/dl and Cr of 2.9mg/dl, showing severe dehydration and then she was referred to our emergency clinic. Fluoroscopy through the ileus tube and an abdominal CT scan showed intussusception and emergency operation was performed on that day. Upon laparotomy, a portion of the jejunum about 25cm distant from the Treitz ligament was invaginated which was caused by a tumor. The invagination was repositioned manually, when two tumors were identified in the jejunum, 25cm and 35cm distant from the Treitz ligament, respectively. The portion of the jejunum involving the tumors was removed. These were well-defined, elastic-soft submucosal tumors with the diameter of about 2cm, each. The histopathological diagnosis was neurofibroma for each tumor. It is etiologically considered that the patient had von Recklinghausen's disease as an underlying disease and her neurofibromas might be secondary to the disease.
