Abstract
We report a case of abdominal aortic aneurysm with congenital factor X deficiency. This deficiency is a rare inherited hemorrhagic disorder. The coagulative disorder was diagnosed prior to a prostate needle biopsy in an 84-year-old male patient. The patient was diagnosed of as having congenital factor X deficiency and prostate cancer. About ten years later, a 60-mm abdominal aortic aneurysm was incidentally found on computed tomography examination for a femoral fracture. Prior to surgery the adequate dose of the combined coagulation factor complex (PPSB-HT®) was determined based on trial results. Graft replacement of the abdominal aorta was undertaken with the administration of PPSB-HT®. In the present case, cardiovascular surgery, which needs heparin administration, was performed successfully ; no abnormal bleeding was observed during or after surgery in this patient with congenital factor X deficiency.